NeurometPlus

Cobalamin F mutation

Incidence

Very rare. Only one case reported. No cases in Saudi Arabia. It is a defect of the cellular metabolism of cobalamin

Clinical Characteristics

Severe neurologic Sx. The reported case had seizures, hyporonia, developm. delay severe.

Precipitants

no

Provocation Tests

no

Diagnostic Procedures

Cobalamin F mutation: EB-F, EB-W, EB-liver, OB-F, GB-F. Definite classification of cobalamine mutations need complementation studies of cultured skin fibroblasts.

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